Lipochoristoma of the internal auditory canal.
نویسندگان
چکیده
PROBLEM Approximately 90% of tumours of cerebellopontine angle and internal auditory canal are vestibular schwannomas (acoustic neuromas) and meningiomas. Lipochoristomas are rare benign masses that represent only 0.15% of cases. METHODOLOGY We report the case of a 39-year-old man who consulted us for right-sided hearing loss and tinnitus. RESULTS Tonal audiometry showed a down-sloping right sensorineural hearing loss in frequencies above 2000 Hz. Magnetic resonance imaging (MRI) revealed a heterogeneous lesion in the right internal auditory canal with areas of hyperintensity on noncontrast T1-weighted MRI and suppression of much of the signal of the lesion with persistence of some areas of enhancement on T1-weighted fat-suppressed images. CONCLUSION Correct imaging diagnosis through MRI (high signal intensity on noncontrast T1-weighted images together with a missing signal in fat suppression sequences) is essential in order to avoid unnecessary surgery or radiation therapy, which are not recommended in the treatment of these lesions.
منابع مشابه
Respiratory Epithelial Adenomatoid Hamartoma: A Very Rare Entity Originating from the External Auditory Canal
Respiratory epithelial adenomatoid hamartoma (REAH) is an uncommon lesion of the upper aerodigestive tract. It is characterized by abnormal glandular formations with ciliated epithelium arising from the nasal cavity, paranasal sinuses and nasopharynx, but other locations have also been described. We did not find any other cases of this hamartomas in the external auditory canal in the literature...
متن کاملLipochoristoma of the Internal Auditory Canal
Neoplasms arising within the internal acoustic canal (IAC) and cerebellopontine angle (CPA) are most commonly of neuroepithelial origin. Vestibular schwannoma represents the most common lesion in the IAC (80–90%) with meningiomas comprising nearly all the rest (10%) of IAC tumors.1–3 Rare tumors include epidermoids, lipochoristomas, and metastatic tumors. Each of these lesions has typical imagi...
متن کاملFirst Branchial Cleft Fistula Associated with External Auditory Canal Stenosis and Middle Ear Cholesteatoma
Introduction: First branchial cleft anomalies manifest with duplication of the external auditory canal. Case Report: This report features a rare case of microtia and congenital middle ear and canal cholesteatoma with first branchial fistula. External auditory canal stenosis was complicated by middle ear and external canal cholesteatoma, but branchial fistula, opening in the zygomatic root and...
متن کاملEnlargement of the Internal Auditory Canal and Associated Posterior Fossa Anomalies in PHACES Association.
We noted enlargement of the internal auditory canal in several of our patients with posterior fossa malformations, hemangiomas, arterial anomalies, cardiac defects, eye abnormalities, and sternal or supraumbilical defects (PHACES) association and hence evaluated children with PHACES for the presence of an enlarged internal auditory canal and potential associated findings, including infantile he...
متن کاملCochlear Dysfunction is not Common in Human Meningioma of the Internal Auditory Canal.
HYPOTHESIS Cochlear dysfunction is not common in human meningioma of the internal auditory canal. BACKGROUND Meningiomas arising from the cerebellopontine angle and internal auditory canal typically cause hearing loss. Cochlear dysfunction is known to contribute to sensorineural hearing loss induced by vestibular schwannoma, the most common tumor of the internal auditory canal. Detailed cochl...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- Journal of neurological surgery reports
دوره 76 1 شماره
صفحات -
تاریخ انتشار 2012